Pediatric Nursing (Nomral) : Psychiatric (Sigmund Freud) Nursing Concept Range Extends To The 18 Month
Pediatric Nursing (Nomral) : Psychiatric (Sigmund Freud) Nursing Concept Range Extends To The 18 Month
Pediatric Nursing (Nomral) : Psychiatric (Sigmund Freud) Nursing Concept Range Extends To The 18 Month
PYLORIC STENOSIS
- Pathology: narrowing of the pyloric sphincter
Anatomy:
- Telescoping or “overlapping” of the small Hirschsprung’s disease, or congenital aganglionic
Stomach: has 2 sphincter – LES/cardiac sphincter (condition on
intestine megacolon, is absence of ganglionic innervation to the muscle
which to affect this portion may include GERD)
- Obstruction of the GI of a section of the bowel—in most instances, the lower portion
- Cardiac sphincter – immature on newborns:
SX: of the sigmoid/descending colon
normal backflow of milk and gastric contents
1. Bile tinged vomitus (when obstuction occurs –
- Minimize this concern through: BURPING No peristaltic waves in this section (CONSTRICTIONS of
vomiting is always present) – green or yellowish
2nd sphincter is the PYLORIC SPHINCTER the affected large instestine) to move fecal material
2. Dehydration
- Narrowing: compromise the passage of food through the segment of intestine.
Assessment:
- Complications include: OBSTRUCTION IS STILL PRESENT
- Fontanels: sunken
SX:
- Skin turgor: (+) 2 sec. (done in the abdomen) for symptoms of aganglionic megacolon generally do not
1. Projectile vomiting – buildup of food
geriatric: sternum become apparent until 6 to 12 months of age
2. Dehydration: vomiting, can be fatal
3. Metabolic Alkalosis SX:
Assessment:
4. SAUSAGE SHAPE – palpation 1.
Vomiting – Fecaloid
- Fontanels: sunken
5. Currant jelly stool – red colored stool (due to 2.
Chronic constipation
- Skin turgor: (+) 2 sec. (done in the abdomen) for
bleeding) 3.
Ribbon like stools (passing through small narrow
geriatric: sternum
6. Colicky pain or intermittent pain is felt segment look like ribbon) and Pellet like stools
3. Metabolic Alkalosis
DX: 4. Portion of the bowel proximal to the obstruction
4. Increase appetite
1. Barium ENEMA dilates, distending the abdomen
5. OLIVE SHAPE – palpation, CONFIRMATORY DX and
Followed x-ray (all barium procedures are proceeded by Factors/Causes:
Hallmark
X- ray): staircase sign higher in the siblings of a child with the disorder
DX:
TX: occurs more often in males than in females
1. Barium swallow caused by an abnormal gene on chromosome 10
The incidence is approximately 1 in 5000 live births 2. Hair color: blonde 5. AKI is present – oliguria as its early manifestation
Assessment 3. Bluish eyes DX:
4. Mental retardation - Newborn screening test
1. meconium cannot pass (infants fail to pass meconium - Beutler test – confirmatory test for the condition
by 24 hours of age and have increasing abdominal 5. Seizures
TX:
distention) 6. Urine: musty order urine –
1. HALT BREASTFEEDING
2. History of constipation or intermittent constipation and HALLMARK/confirmatory order of the patient - Formula feeding is done instead: NUTRAMIGEN
diarrhea. urine
3. Gloved finger is inserted into the rectum, the rectum is
empty because fecal material cannot pass into the DX:
rectum through the obstructed portion 1. Newborn screening Test: PKU screening test – collected
DX: CLEFT LIP
in the heel of the baby.
1. A barium enema is generally ordered to substantiate - Taken in 24-72 hours of the birth
the diagnosis. 2. Guthrie Blood test – confirmatory test for PKU
- X- ray: pigtail sign TX:
Note: The barium will outline on x-ray film the narrow, nerveless 1. Newborn with PKU – breastfeeding is NOT ALLOWED –
portion and the proximal distended portion of the bowel. A formula is used: LOFENALAC
barium enema must be used cautiously, however, because
children cannot expel this afterward any more effectively than
they can stool
2. Definitive diagnosis is by a biopsy/anorectal
manometry
TX
1. Resection of the affected section, with anastomosis of
the intestine (termed a pull-through operation) The maxillary and median nasal processes normally fuse
2. Newborn by two-stage surgery: between weeks 5 and 8 (first trimester) of intrauterine life.
2.1 first a temporary colostomy is established
2.2 bowel repair for 12-18 months of age CLEFT LIP is where fusion fails to occur, causing to range from a
2.3 In the few instances in which the anus is small notch in the upper lip to total separation of the lip and
deprived of nerve endings, a permanent facial structure up into the floor of the nose, with even the upper
colostomy will be established. teeth and gingiva absent
deviation may be unilateral, bilateral and medial type
Metabolic Disorders nose is flattened because the incomplete fusion of the
upper lip has allowed it to expand in a horizontal
dimension
PHNENYLKETONURIA Sucking problem
GALACTOCEMIA
- Inc. phenylalanine or TOXIC LEVELS in the
- Inc. galactose – more fatal
blood stream - Affects the CNS, eyes, liver and the kidneys Cleft lip is more prevalent among boys than girls
- CNS is affected: brain damage – mental Manifestations: Causes
retardation 1. CNS: mental retardations familial tendency/transmission of multiple genes
- Newborn screening test detection 2. CNS: seizures Teratogenic factors (second month of pregnancy is
SX: 3. Eyes: congenital cataracts MOST DAMAGING FOR teratogenic factors) present
1. Melanin lvl is low (light or white or fair skinned 4. Skins: increase bilirubin release results in the jaundice: during weeks 5 to 8 of intrauterine life
due to its absence) “GOLDEN BOY” o viral infection
o deficiency of folic acid Therapeutic Management one of the first types of congenital heart disease
o TORCH: Toxoplasmosis, Other agents ex. 2. early repair described
Hepatitis, syphilis, Rubella (small viral dimensions - (Increases speech development, results in a children with this disorder show a deletion abnormality
hence teratogenic compared to Rubeola) , necessary second-stage repair as the child’s of chromosome 22 (22q11.2)
Cytomegalovirus, Herpes simplex palate arch grows) the disorder can result from a documented
Assessment 3. two-stage palate repair (Malek Protocol)
chromosome disorder
Inspection (needs good lighting) - (Soft palate repair at 3 to 6 months; hard palate
It is called a tetralogy because four anomalies are present:
sonogram repair at 15 to 18 months)
4. follow-up treatment by a pedodontist, or a dentist 1. pulmonary stenosis – narrowing
TX: - (For extractions or realignment of teeth to detect 2. VSD (usually large)
Parents of a child should be referred for genetic if speech or hearing difficulty occurs) 3. Dextroposition (overriding) of the aorta
counseling to ensure they understand that they NX for post - op: 4. hypertrophy of the right ventricle
have about a 4% chance of having another child 1. DO NOT LET THE PATIENT OR THE BABY CRY – ruined NOTE: ASD may be present as the 5th condition
with a cleft lip or palate or future children are at a sutures Pathology:
greater risk than usual for this problem - Attend to needs of the baby ex. Food Because of the pulmonary stenosis, pressure builds up
Fetal surgery (for cleft lip discovered while the - Racking, cuddle – to minimize the cry of the baby in the right side of the heart. Blood then shunts from this area of
infant is still in utero) Note: DO NOT USE PACIFIER TO THE INFANT – pre-op is allowed increased pressure into the left ventricle and the overriding
Surgical repair (between 2-10 weeks of age which is since patient is NPO aorta. The extra effort involved to force blood through the
a better age for surgical risk) – cheiloplasty: side 2. NO straw and NO use of spoon stenosed pulmonary artery causes the fourth deformity,
lying 3. Use breck feeder, dropper is used most commonly in
hypertrophy of the right ventricle.
nasal mold apparatus applied before surgery to the Philippines.
shape a better nostril 4. Elbow restrained may be used – tongue depressor, or
mommy restraint SX:
nasal rhinoplasty to straighten a deviated nasal
1. HYPOXIA
septum (4 to 6 years of age)
2. may not exhibit a high degree of cyanosis immediately
Early repair helps infants experience the pleasure
of sucking after birth, becoming more active, however, their skin
CLEFT PALATE acquires a bluish tint as cyanosis begins -
The palatal process closes at approximately weeks 9 to 12 of HYPERCAPNIA
intrauterine life. 3. polycythemia
CLEFT PALATE is considered an opening of the palate usually on Complication:
the midline; may involve the anterior hard palate, the posterior thrombophlebitis
soft palate, or both embolism
Degree: It may be a separate anomaly, but as a rule it occurs in cerebrovascular accident
conjunction with a cleft lip 4. If the condition is not corrected: development of
tends to occur more frequently in girls than boys severe dyspnea, growth restriction, and clubbing of the
speech problem fingers
Causes
5. Assume a squatting or a knee–chest position when
polygenic inheritance
resting (provides physiologic relief, if not done the
environmental influences
heart can be overwhelmed)
Assessment
Inspection (must have good lighting) Develop syncope (fainting) and hypercyanotic
depressing the newborn’s tongue with a tongue blade episodes (sometimes called Tet spells).
must be assessed for other congenital anomalies
TETRALOGY OF FALLOT
6. A loud, harsh, widely transmitted murmur or a soft,
scratchy localized systolic murmur in the left second,
third, or fourth parasternal interspace may be present
Note: Follow prolonged crying or exertion. They can be so extreme, if long term,
that children develop cognitive challenge
DX:
history
physical symptom
2D echo/ echocardiography: BOOT SHAPED HEART
ECG
cardiac catheterization
laboratory findings: polycythemia, increased Hgb, Hct,
and total RBC as well as reduced oxygen saturation
TX:
1. If a baby begins to have a hypoxic episode:
administering oxygen
placing the baby in a knee–chest position
2. Administering morphine sulfate generally reduces
symptoms.
3. If not, propranolol (Inderal, a beta-blocker) may be
given orally to aid pulmonary artery dilation.
4. A temporary or palliative surgical repair, called the
Blalock-Taussig procedure, can create a shunt between
the aorta and the pulmonary artery (creating a ductus
arteriosus)
This will allow blood to leave the aorta and
enter the pulmonary artery, oxygenate in
the lungs, and return to the left side of the
heart, the aorta, and the body
When a Blalock-Taussig procedure is done, a
child will not have a palpable pulse in the
right arm after this procedure. For this
reason, blood pressure and venipuncture
should be avoided in the affected arm
5. Brock’s procedure – curative procedure
- Widening of the pulmonic valve, Dacron patch is
inserted