Location via proxy:   [ UP ]  
[Report a bug]   [Manage cookies]                

eEMCASE - MAR Letak Rendah Tanpa Fistel

Download as pptx, pdf, or txt
Download as pptx, pdf, or txt
You are on page 1of 22

EMERGENCY CASE REPORTS

Wednesday, August 26th 2020


SURGERY DEPARTMENT

EMERGENCY ROOM
Wahidin Sudirohusodo General Hospital
Makassar
Name : Ch. EE Age : 2 days
RM : 893594 DPJP : dr. UM
BW : 3600gr

CHIEF COMPLAIN : No Anal Canal


HISTORY TAKING : This condition has been present since the baby was born. There wasn’t history
of vomiting, fever and seizure. There wasn”t history of dyspnea or cyanosis
when the baby crying. There wasn’t history of same disorder in the family.
History of maternal pregnancy : the patient was born normal pervaginam
assisted by midwife with gestational age 39 weeks, birth weight 3600 grams
and APGAR score 8/9. During pregnancy the mother controls the ANC
routinely at the doctor PKM, there wasn’t history of ultrasound check. There
was no history of drugs or herbs consumed during pregnancy. The patient was
referred from RSUD Majene.

MICTURATION : Via urethra, 0,5cc/KgBB/Hours, yellow, no feces


DEFECATION : No anal canal
PHYSICAL EXAMINATION
GENERAL STATUS:
Active / well-nourished / compos mentis / BW 3600 grams

VITAL SIGN:
HR: 136x/min RR: 30x/min T(Ax): 36.8°C

HEAD & FACE:


Conjunctiva anemic (-), sclera icteric (-), large fontanel drops (-), dry lips
and mouth mucosa (-), perioral cyanosis (-), hypersalivasi (-)

THORAX :
Symmetric
Lungs : Equal Bronchovesikuler Breath Sound , Ronchi :-/-, Wheezing: -/-
Heart : Regular Heart Sound , Murmur : -
PHYSICAL EXAMINATION
ABDOMEN
I : convex, distended, follow breath motion, skin color was the
same with its vicinity, darm contour (-), darm steifung (-)
A : peristaltic sound was increased
P : Soefel (+)
P : tympani
PHYSICAL EXAMINATION
Anal Region
I : Anal canal (-)
Bucket handle (-)
Anal dimple (+)
Fistule (-)

Genital Region
Seen OUE in the distal of penis
Meconium (-)
DEHYDRATION STATUS

• Head Fontanel: normal


• Eye: normal
• Lip/Mouth: moist
• Turgor: normal
CLINICAL DIAGNOSIS

Anorectal Malformation With No Fistula


Without Dehidration
LABORATORY RESULT
WBC : 10,1 x 103 /μL Natrium : 144 mmol/L

RBC : 4,58 x 106 /μL Kalium : 3,4 mmol/L

HGB : 15,6 g/dL Chlorida : 105 mmol/L

HCT : 52 % SGOT : 61 U/L

PLT : 160 x103/ µl SGPT : 15 U/L

PT/ aPTT : 33,7 s / 46,1 s IgM & IgG : Non Reactive

INR : 3,69

Blood Sugar : 75 mg/dl

Ureum : 33mg/dl

Creatinin : 1,30 mg/dl


CROSS TABLE LATERAL KNEE-CHEST POSISI X-RAY
BABY GRAM
WORKING : - Low Level Anorectal Malformation With No
DIAGNOSIS Fistula
-Without Dehidration
-Lengthening of The Hemostasis Function

MANAGEMENT : • IVFD Asering


• (Maintenance 3,6 x 100 = 360cc/24 hours)
• Insert OGT
• Insert Urinary catheter
• Consult to NICU
(Infant warmer care, stop intake oral, parenteral
nutrition, antibiotik, Inj Vit. K 1mg/IM)
• Plan for Limited PSARP (Anoplasty)
THANK YOU
USG PERINEUM
WHO Dehydration Classification
ANATOMI

• Oldham K, Colombani P, Foglia R, Skinner M. Rektum and Anus. In: Principles and Practice of Pediatric Surgery Vol.2. Philadelphia: Lippincott Williams & Wilkins, 2005;
p.1395-1434
https://www.grepmed.com/images/1
710/association-pediatrics-diagnosis-
anomalies-vacterl-peds
KLASIFIKASI
Penggolongan Anatomi Malformasi Anorektal menurut Sjamsuhidayat (Laki-laki)

Golongan I : Tindakan :
1.Fistel urine Kolostomi neonatus pada usia
2.Atresia rekti 4-6 bulan
3.Perineum datar
4.Tanpa fistel udara> 1cm dari kulit pada
invertogram

Golongan II : Tindakan :
1.Fistel perineum Operasi definitif neonatus
2.Membran anal tanpa kolonostomi
3.Stenosis ani  
4.Bucket handle  
5.Tanpa fistel, udara < 1 cm dari kulit pada  
invertogram

• Oldham K, Colombani P, Foglia R, Skinner M. Rektum and Anus. In: Principles and Practice of Pediatric Surgery Vol.2. Philadelphia: Lippincott Williams & Wilkins, 2005;
p.1395-1434
PSARP
PSARP dibagi menjadi tiga yaitu minimal, limited, dan full PSARP

MINIMAL LIMITED

Minimal PSARP tidak Limited PSARP yang FULL


dilakukan pemotingan dibelah adalah otot
otot levator maupun sfingter eksternus, Full PSARP dilakukan
vertical fibre, yang muscle fibre, muscle pada atresia ani letak
penting adalah complex, serta tidak tinggi, pada fistel
memisahkan common memotong levator. rektovaginalis, fistel
wall untuk Dan dilakukan pada rekto uretralis, atresia
memsahkan rektum atresia ani dengan rektum, bladder neck
dengan vagina dan fistel rektovestibular dan stenosis rektum
dibelah hanya otot
sfingter eksternus
perineal
• Van der steeg, H. J. J., et al. European consensus meeting of ARM-Net members concerning diagnosis and early management of newborns with anorektal
malformations. Techniques in coloproctology, 2015, 19.3: 181-185.
• Bischoff, A., Bealer, J., & Peña, A. (2017). Controversies in anorektal malformations. The Lancet Child & Adolescent Health, 1(4), 323-330.
TEKNIK OPERASI
Dilakukan dengan general anestesi,
Stimulasi perineum dengan alat
dengan intubasi endotrakeal,
Pena Muscle Stimulator untuk
dengan posisi pasien tengkurap dan
identifikasi anal dimple.
pelvis ditinggikan.

Dibelah jaringan subkutis, lemak, Insisi bagian tengah sakrum kearah


parasagital fiber dan muscle bawah melewati pusat spingter dan
complex. berhenti 2 cm didepannya

Os koksigeus dibelah sampai tampak


muskulus levator, dan muskulus Rektum dibebas dari jaringan
levator dibelah tampak dinding sekitarnya
belakang rektum

Rektum ditarik melewati levator,


Dilakukan anoplasti dan dijaga
muscle complex dan parasagital
jangan sampai tension.
fiber.

• Bischoff A, Dickie BH, Levitt MA, Peña A. Anorektal Malformations. Pediatric Surgery. 2017:1-27.
POST OP DIAGNOSIS : - Low Level Anorectal Malformation With
No Fistula
- Without Dehidration

FOLLOW UP : • Vital sign


• Wound care

PROGNOSIS : Good

You might also like