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Journal of Pharmacy and Pharmacology
Pentalogy of Cantrell with Total Ectopia Cordis and a Major Omphalocele—A Case ReportFrontiers in pediatrics
Cantrell Syndrome-A Rare Complex Congenital Anomaly: A Case Report and Literature Review2018 •
Cantrell syndrome (CS) or pentalogy of Cantrell is defined as a rare condition involving a midline anterior abdominal wall defect, a distal sternal cleft, a defect of the anterior diaphragm, and a defect of the apical pericardium with pericardio-peritoneal communication, as well as intracardiac anomalies. We report the case of a male newborn with type 2 CS diagnosed during intrauterine life based on ultrasonographic evaluation. Clinical examination at birth revealed an abdominal wall defect with extrathoracic displacement of the heart and a diastasis of the sagittal suture. Postnatal echocardiography revealed tricuspid atresia, partial extrathoracic and extra-abdominal displacement of the heart and liver, a large ventricular septal defect, severe subpulmonary stenosis, hypoplasia of the pulmonary artery, and a large hourglass-shaped left ventricle secondary to narrowing of the heart at the level of its extrathoracic displacement. Computed tomography showed additional abnormalities i...
Ultrasound in Obstetrics and Gynecology
Changing findings in pentalogy of Cantrell in fetal life2008 •
Pentalogy of Cantrell is the association of five features: a midline anterior ventral wall defect, a diaphragmatic defect, a cleft distal sternum, a defect of the apical pericardium with communication into the peritoneum, and an intracardiac defect. This is a complex abnormality that requires multiple surgical procedures, but which can be successfully treated postnatally with staged surgery. Three recent cases demonstrated features in prenatal life that were unexpected to us, and which we felt were worthy of description. The diagnosis of the pentalogy of Cantrell was made at 11, 16 and 14 weeks. Two of the three had an increased nuchal translucency measurement. All three fetuses had a major abdominal wall defect with a significant degree of protrusion of the cardiac ventricles outside the chest at the initial scan. At 20 and 26 weeks, the heart was seen to be within the chest with no protrusion, even of the apex. An intracardiac malformation was found prenatally in two of three cases. There were no karyotype anomalies and all three cases survived despite multiple operations. At the time of writing they were aged 2, 5 and 8 years. The ultrasound findings in all three cases showed an evolving pattern during gestation, with a greater degree of protrusion of the heart through the lower sternal defect into the exomphalos in the early scans than was present later. The possibility of an improvement in the findings has some bearing on counseling in early pregnancy in this complex condition.
Journal of clinical neonatology
Pentalogy of cantrell: an extremely rare congenital anomaly2013 •
A baby with the complete form of pentalogy of Cantrell was delivered at 33 weeks of gestation. The hallmark of this syndrome is ectopia cordis (EC) with omphalocele. Even though a fetal diagnosis was made at 14 weeks, parents have decided to continue with the pregnancy. Early antenatal ultrasonographic diagnosis is essential as survival depends mostly on the EC, associated cardiac anomalies and degree of thoraco-abdominal defect. Fetal diagnosis of this lethal anomaly before viability gives the parents an option of termination.
Journal of Pediatric Surgery Case Reports
Pentalogy of Cantrell: Complete expression with mediastinal teratoma2015 •
Pediatric and Developmental Pathology
Pentalogy of Cantrell: A Case Report with Pathologic Findings2004 •
2006 •
Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic-to-pulmonary anastomosis and uneventful recovering.
Napoleone duecento anni dopo, a cura di Daniele Paci Fumelli e Marco Rocchi
Napoleone a Pesaro e nelle Marche2021 •
Pinturas rupestres esquemáticas de Calorzo, Cebreros, Avila
Pinturas rupestres esquemáticas de Calorzo, Cebreros, Avila2024 •
Revista Cuicuilco Volumen 9, N° 25, mayo-agosto 2002. Número especial: Análisis del discurso y semiótica de la cultura: perspectivas analíticas para el tercer milenio. Tomo II. (Versión ampliada)
Entre el giro lingüístico y el guiño hermenéutico: tópicos y competencia en la semiótica musical actual2002 •
Literatura infantil para el desarrollo de la creatividad en niños de educación preescolar
LITERATURA INFANTILStudia Ecologiae et Bioethicae
Semantyczno-pragmatyczne znaczenie natury2008 •
Jundishapur Journal of Natural Pharmaceutical Products
The Effects of Doxorubicin, Ethanol Extract and Flavonoid-rich Fraction of Euphorbia Splendida Mobayen on the PARP Level, and APC Gene Expression in HT-29 Human Colon Cancer Cell Line2020 •
2018 •
The Lichenologist
Candelariella blastidiata sp. nov. (Ascomycota, Candelariaceae) from Eurasia and North America, and a key for grey thalli Candelariella2017 •
Recent Advances in Environmental Science from the Euro-Mediterranean and Surrounding Regions
N-Doping Effect on the Activity of TiO2 Supported Catalysts in Glycerol Oxidation2018 •
T. Dokument 37
Initiating information services in a developing country - a case from Tanzania, and some generalizations1981 •
Le Verger - Bouquet XXVIII : Comment aborder l'étude des minores ? dir. Anne-Gaëlle Leterrier Gagliano et Lionel Piettre avec la collaboration d’Adeline Lionetto
Des minores au sein d’un (plus) grand genre : le rôle des occasionnels dans quelques Mémoires du XVIe siècle2024 •